Lymphoblastic cutar sankarar bargo

Idan tsarin ciwon hematopoiesis yana damuwa a cikin kututtukan kasusuwa, yawancin kwayoyin da basu riga sun kira ba, ana kira lymphoblasts. Idan sun kasance sun zama lymphocytes, amma sunyi mummunan, cutar kututtukan lymphoblastic mai tsanani ya karu. Kwayar cutar tana nuna saurin maye gurbin ƙwayoyin jini na yau da kullum tare da clones, kuma zasu iya tara ba kawai a cikin kasusuwan kasusuwa da kyallen takarda ba, har ma a cikin sauran kwayoyin.

Sanin asali na m lymphoblastic cutar sankarar bargo

Sakamakon binciken da ake amfani da ita na samar da sinadarin jini ya dace da raguwa da aikin dukan kwayoyin. Rashin ƙananan ƙwayoyin kwayoyin halitta (lymphoblasts) yana haifar da shigarwa zuwa cikin ƙwayoyin lymph, yalwata, hanta, lalacewar tsarin kulawa na tsakiya. Bugu da ƙari, ƙayyadadden yanayin cutar ya haɗa da canje-canje a cikin aikin ɓawon launin fata. Ya dakatar da samar da isasshen yawan jinin jini, platelets da leukocytes, ya maye gurbin su tare da clones na farko tare da maye gurbi.

Dangane da irin kwayoyin cutar da ke ɗauke da ciwon daji, ƙananan cutar T-cell lymphoblastic (T-cell) da B-linear suna bambanta. Irin wadannan nau'o'in na faruwa sau da yawa sau da yawa, a cikin kimanin 85% na lokuta.

Muraya cutar sankarar lymphoblastic mai tsanani - haddasawa

Dalilin da ya haifar da ci gaba da cutar da aka bayyana shi ne canje-canjen da ba a canzawa a cikin chromosomes. Ba a tabbatar da ainihin dalilai na wannan tsari ba, hadarin cutar sankarar bargo na irin wannan ya faru a cikin wadannan lokuta:

Murayacciyar lymphoblastic mai laushi - bayyanar cututtuka

Ɗaya daga cikin siffofin alamun da aka gabatar shi ne wanda ba shi da cikakkun bayanai game da alamun bayyanar. Sun kasance sau da yawa kama da halaye manifestations na sauran cututtuka, saboda haka yana yiwuwa a gane asibiti cutar sankarar bargo kawai bayan jerin dakin gwaje-gwaje gwaje-gwaje.

Matsaloli da ka iya yiwuwa:

Muraya cutar sankarar lymphoblastic mai raɗaɗi - magani

Makirci mai mahimmanci ya ƙunshi matakai uku:

  1. Na farko shi ne babban kumburiyo tare da cytostatics, glucocorticosteroid hormones da anthracyclines. Wannan yana ba da dama don samun nasarar gyara cutar - rage abun ciki na lymphoblasts a cikin kasusuwan kasusuwan zuwa kashi 5%. Tsawon lokacin gyaran gyarawa yana kusa da makonni 6-8 bayan an tabbatar da ganewar asali.
  2. A mataki na biyu na magani, chemotherapy ya ci gaba, amma a ƙananan allurai, don ƙarfafa sakamakon da halakar sauran kwayoyin da suka rage. Wannan yana ba ka damar dakatar da cutar sankarar lymphoblastic mai tsanani kuma ya hana sake dawowa cutar a nan gaba. Jimlar lokacin da aka ɗauka ta kasance daga watanni 3 zuwa 8, daidai likitan ya ƙayyade daidai lokacin da likitanci ya dace daidai da cutar cutar sankarar bargo.
  3. Mataki na uku ana kiran taimako. A wannan lokacin, yawanci ana biye da hanya da 6-mercaptopurine. Duk da tsawon lokaci na karshe na farfadowa (shekaru 2-3), an jure shi da kyau, tun da yake bazai buƙatar samun asibiti - duk wanda ya yi haƙuri ba zai karbi Allunan ba.